Amyotrophic sclerosis lateral: take, tohu, maimoatanga

"Amyotrophic sclerosis lateral" mate ko te māuiuitanga organic taimaha o te etiology unknown. Kei te āhuatanga i te reira e te pāpaka o nga neurons nekeneke o runga me raro, akoranga ahu whakamua. Mutu ALS (Amyotrophic sclerosis lateral) noa'i te mate. Next, ako matou pehea ki te whakaatu māuiuitanga, a ahakoa i reira ko te taea o te pae whakakahoretia o te mate.

Overview

whakaaro Amyotrophic sclerosis lateral te he mate kihai i taea. pānga te reira i te pūnaha io pokapū. He māuiuitanga etahi ingoa atu: mate Lou Gehrig o, mate Louis Gehrig o, mo te tauira. e kore te mea ngāwari tonu te tātaritanga. Ko te take i roto i nga tau tata nei tino nui haere whānuitanga o ngā ma'i i roto i te mau faaiteraa haumanu rerekē e kitea kahore pīari rite taua, a Amyotrophic syndrome sclerosis lateral. I roto i tenei whakaaro, tohunga o tenei ra whakapono te tohu mahi tino nui, me te whakamahine o mate etiology.

Amyotrophic Lateral Sclerosis: Tohu

E pā ana Faaiteraa o māuiuitanga, matua, ki te hinga o te raro nekeneke neuron. sclerosis lateral Amyotrophic, ngā atrophy, ngoikore, fasciculations nei tohu, he tohu o te kino teihana corticospinal. He spasticity me nui haere iohere me te whakamutunga reflexes pathological kahore waimaerotanga rongo. I roto i tenei take, kia whai wāhi te mau api parau cortico-bulbar. Tenei, i roto i te tahuri, ka whakatere i te whanaketanga o te māuiuitanga i te taumata o te brainstem. ALS pā tangata pakeke. e kore te māuiuitanga whakawhanakehia noa te tau o 16.

whakaatu āhuatanga

I roto i te tangata e mate ana i te sclerosis lateral Amyotrophic, nga tīmatanga o te mate, ko te tohua atrophy uaua (akoranga ahu whakamua) ki hyperreflexia. Tēnei āhuatanga ko te faaiteraa haumanu tino nui. Ka taea e māuiuitanga timata ki te whanake ki te weu uaua katoa striated. Ka taea e Amyotrophic sclerosis lateral i te maha o ngā momo: bulbar, tiketike, lumbosacral me waha-rei. Meinga o te mate, ka rite ki te tikanga, ko reira te mate o te uaua romahā i muri e pā ana ki 3-5 tau. He maha ngā āhuatanga āhuatanga Amyotrophic sclerosis lateral. Ko tētahi o nga mau faaiteraa tino auau whakaaro ngoikore ahu whakamua o nga weu uaua o tetahi o nga topito o runga. Tikanga, ka tīmata i te reira i te ringa. Ki te whanaketanga o te rere kiko māuiuitanga ahua proximally tikanga ko atu pai. I te timatanga o te mate e pā ana ki te whanaketanga o te ngoikore uaua i roto i te ringa, whai wāhi te tukanga thenar muka. E whakaatu ana Tūnga adduction ngoikore (mauria mai) me te pato'iraa o te koromatua. He uaua ake te hua ki te taa i te koromatua, me te maihao, ohorere mana nekeneke pai. Tūroro ki ALS ite uaua te whakauru (buttoning-iho), me te tiki ake taonga iti. Ki te pānga ki te ringa tino puta fifi ka tuhituhi, ngā mahi ia rā i roto i te kāinga. Āhua pai puka lumbosacral whakaaro.

Ko te māuiuitanga angamaheni mo

I roto i tenei take i reira ko te kainga, whai wāhi mǎrû i te tukanga o te uaua o te alangá kotahi. I muri mai ka timata te reira ki te horapa i te ringa tuarua ki te hinga weu bulbar waewae ranei. kia timata Amyotrophic sclerosis lateral ki uaua arero, mangai, mata ranei waewae. I roto i tenei take, i te whakangaromanga muri "kore e te hopu ake" te taketake. I roto i tenei whakaaro, whakaaro reira te tümanako ora poto i te puka bulbar. mate tūroro, toe tata i runga i te waewae, e kore e tatari hoki raro pāpāngia e alangá.

whanaketanga atu

sclerosis lateral Amyotrophic tahi e ngā ngā o te tohu o te pāpāngia (bulbar me pseudobulbar). pai io whakakitea tenei dysphagia, me dysarthria, a muri mai me disorders romahā. whakaaro te āhuatanga āhuatanga o tata katoa momo o te mate e ki he whakapakari wawe o te pūpū kauae. A, no te horomia ake pinepine kitea te dysphagia kai wai atu i ki totoka. I te wa ano, kia tuhia te reira e te whakamahi o te muri i roto i te akoranga o te mate haereraa riro uaua atu. He he he ngoikore i roto i te uaua masticatory, tīmata Hawaiki ngao ngohengohe, riro atrophic me whakaritea te arero. tīmata tahi Amyotrophic sclerosis lateral e te rere tonu o te huware, anarthria. riro te reira i taea ki te horomia, e faarahi te reira i te tūponotanga o te wawata kakā. Me mahara hoki käore te reira e kua korerotia nga cramps (cramps taratahi i roto i te kuao kau) i roto i ngā tūroro katoa, a ka kua maha whakaaro nga tohu tuatahi o te mate.

Tohatoha o atrophy

kia mea ahau e he reira kaua whiriwhiri. I nga ringa o te manawanui tuhipoka hinga hypothenar, thenar, interosseous me deltoids. I waewae whakawhanake atrophy i te wāhi o te raveraa i dorsiflexion. O ngā uaua bulbar pakaru kiko o te mangai ngohengohe me te arero. E whakaaro weu Oculomotor te tino ātete ki te atrophy.

ngā kitenga ā-

I roto i te māuiuitanga o disorders onge me sphincter. Ko tētahi o nga āhuatanga mīharo o te mate ko te kore o keha te pēhanga i roto i te pararutiki hoki te wa roa tūroro ro'i. kitea ano e reira e puta tupu ina he tino onge mate. Te kore whakapono anake i te torutoru iti-rōpū: ko te hapu me te puka matatini "AD sclerosis parkinsonism-tupu." Whakaahuatia rite wā e pā ana i te kākahu o raro ranei neurons nekeneke runga. kia taea tenei hinga tetahi kotahi rohe. Hei tauira, kia mamae kaha runga neuron nekeneke. I roto i tenei take korero tatou o sclerosis lateral tuatahi. Anö kino taea te kitea i roto i te neurons nekeneke raro. I roto i tenei take korero tatou o perednerogovom syndrome.

rheotachygraphy

Ko tenei tikanga o ngā uara tātaritanga roto tikanga paraclinical o ako mate. Mā te EMG heheu pūtau whānui kino mārōrō haona (tae atu i roto i te rongoa (hauora) uaua) ki fasciculations fibrillation, huringa i roto i te moe, o wae nekeneke, he ngaru pai ki te tere tonu o te whakatö o te weu excitation i roto i raru tairongo.

tātaringa

Ki te whakahaere rangahau ki te tautuhi i te māuiuitanga, me whai koe i:

• Tohu o te kino ki te neurons nekeneke raro. he tika, i roto i ngā reira, a EMG haamauraa ora (hauora) uaua
• Tohu o runga kino nekeneke neuron i roto i te akoranga whakamua.

Hoki te tātaritanga me kore:

• disorders Sphincter.
• raruraru rongo.
• mate a Parkinson.
• Visual waimaerotanga.
• Bass tāwhai te mau faaiteraa.
• Tupu o te momo Alzheimer.
• disorders Autonomic.

whakapumautia tātaritanga te fasciculations i roto i te 1 atu ranei rohe, tohu EMG tere noa o te whakatö o te tairongo excitation me muka nekeneke. I roto i te kāwai kia tuhia:

• Haumaru ki ALS. He take i roto i te wāhi mai ki te kitea tohu o te whara i roto i te raro neurons pūkaha me te tihi toru ngā wāhanga o te tinana.
• Pea. I roto i tenei take, i reira he tohu o te lesion i roto i te raro, me te runga neurons nekeneke me i rua ngā wāhi o te tinana.
• Pea. whakakitea pāpaka tohu o runga me raro neuron nekeneke i roto i tetahi rohe o te tinana ranei, ki te kia pakaru i roto i te rua o nga rohe 2-3. I roto i te take whakamutunga e korero tatou e pā ana ki te mau faaiteraa o ALS i kotahi alangá, pararutiki bulbar ahu whakamua, me te puka tuatahi.

Maimoatanga o te sclerosis lateral Amyotrophic

I teie mahana te tarukino tuatahi me anake whakamahia i roto i te māuiuitanga, ko te tikanga o "Riluzole". Kei te whakaaetia te reira i roto i Europe me te US, engari i roto i Russia e kore e rēhitatia me kore e taea te tūtohu e te tākuta mōhiohio. e kore e rongoā whakakore i te mate. Ko ko reira anake te tarukino e he pānga pai i runga i te tümanako ora o tūroro. Ko te medicament "Riluzole" tauturu whakaiti i te kukū o te glutamate (neurotransmitter i roto i te CNS), tukua i roto i te wahi o te pana io. Kua kitea tētahi taikaha o tenei pūhui kua i roto i te kitenga mahi kino i runga i neurons filosilivá me te roro. E ai ki nga hua o te rangahau haumanu kitea e ora te hunga e ka mau te rongoā, he toharite o 2-3 marama roa atu te hunga e whakamahia te placebo.

antioxidants

Tenei piha o pūhui matūkai āwhina ki te ārai kino ki te tinana e taea meinga Radicals free. Kei te whakapono te reira e kia he tangata ki ALS kia ngoikore ake ki o ratou pānga kino. I teie mahana, e tīmata ki te tāutu i, kitea pānga tāpiringa hua kei roto antioxidants akoranga. Ētahi o ēnei hua kua haere te whakamātautau, i taka ki te whakamatau i tona whai huatanga.

therapy te rere

tauturu i Various mahi hanga ora māmā hoki ki te tūroro kia reira whakamarie atu. I roto i ngā, e korero tatou e pā ana ki te whakangā. Kei te whakapono te reira e reflexology, aromatherapy me te mirimiri te āwhina faaore ahotea, me te whakaiti i manukanuka, wātea uaua, māori o toto, me te te tīpona tohanga. tauturu i ēnei ngā tukanga ki te pehea o te mamae e tika ana ki te ariā o kaipatu mamae endogenous whakaputaina e te tinana me endorphins. e rongoā ranei tetahi tukanga ranei kia tūtohutia e te tākuta. I roto i te Amyotrophic sclerosis lateral whaiaro rongoā-kore te tino tūtohutia.