HauoraDiseases me ngā Here

Mate Farah. Take, te tātaritanga, maimoatanga

i whakaahuatia tuatahi mate a Farah i te 30raa o te rau tau rua tekau. Ko te mate riro (kaka calcification iaia) tenei. I roto i te nuinga o te wā kia huaina rōpū o pathologies i ai nga rohe pāngia o nga oko roro, me te toto. E takoto tai konupūmā i roto i nga taiepa o te iti pera, tōiti. puta Farah syndrome huri noa te tau o 40-50 tau, engari i reira he take, me mua ona mau faaiteraa.

He rōpū o mate neurodegenerative

Tenei rōpū o mate āhuatanga e te pūnaha io pokapū. He etahi maha o neurons mate, e tika ana ki te disorders neurological. Ka taea e whai mate Neurodegenerative take rerekē, me te rerekē faaiteraa haumanu. Ko reira nui e mate katoa i roto i tēnei kāwai e mahu. therapy katoa, whakamahia nei te, he symptomatic. Ko, whakahaere reira te whakakitenga o te mate, engari e kore e whai wāhi ki te mahi whakaora i o ngā wāhi pakaru. e kia neural kiko transplantation, Heoi, kua rua tutukitanga hangarau, me te morare i te tikanga te whai hua te nuinga. Hoki taua mate ngā mate o Alzheimer, Parkinson o, Farah. Tikanga, te tātaritanga o mate i roto i te wāhanga wawe utrudnena. Nuinga o ngā wā i roto i te tātaritanga o ngā tohunga i runga i amuamu manawanui me ngā kitenga o ratou whanonga. Ko te taputapu matua ko te scan (computed, te kōwarotanga autō).

tohutanga o te mate

Mai te mate - he āhuatanga onge, ki nga tohunga uaua whakarato i te pikitia haumanu tika o te syndrome. kia puta Tohu ki te he pakeke atu i te 40 tau te manawanui. I roto i te iwi teina kia peroo me wara Tīmata tohu o te mate. whakaohooho Tūroro ruruku o nekehanga, parkinsonism. Ano i runga i te whanaketanga o te mate kia tohu tohu pērā i faaati, dystonia, nekehanga e alangá tere, me te kōhikohiko (chorea), contractions tumu o te ringa, waewae. Mai pānga te mate ngā wāhanga o te roro, te heke kaha mahi, aravihi hinengaro. Hoki mamae me te mahara o te tangata. E mea pinepine takahi a reira. kia ngā Ētahi atu tohu neurological mamae, disorders hinengaro. Wehewehe i te puka punua o te mate, i faaite ake i roto i ngā tamariki, ngā taiohi. Ko te tohu matua i roto i tenei take e whai ake nei: dystonia, chorea, haurangi o haurangi. he āhuatanga hoki waenganui me te pakeke te tau puka taipāpā. I roto i tenei take, i reira he parkinsonism, mate kupu, ētahi atu raruraru i roto i te pūnaha io. Hoki kia taikaha mimi.

take ka taea o te syndrome Farah

e kore e whakapumautia pai te take no te mea o e ai whakawhanake i te mate. Heoi, kua mohiotia ai e te pānga nui i runga i tona putanga he disorders o te thyroid, repe parathyroid. A, no te tupu rahunga i roto i tenei konupūmā tukanga hei utu, ūkuikui. Ka taea e taua mate neurodegenerative puta i roto i disorders o waikawa-turanga toenga i roto i te tinana. Alkalosis, ārahi ki te mate nui o te waikawa. Ko te hakari pūhui kawakore i roto i te taikaha. He he ano hoki te tirohanga e whakakitea te syndrome e i roto i Farah ngā ira mate. mutated Ko te ira e te kawenga mo te utu o taua āhuatanga rite konupūmā. Heoi, i tenei putanga he rota o ngā whakahēnga. Kia mohiotia take taratahi, ka whakakitea tohu o te mate i muri i irradiation o te matenga, tāoke poisoning, mata, i roto i ngā tamariki ki Down syndrome. Ano, pāngia calcification i roto i te tangata, kōpukupuku (onge). Ko tētahi atu take ka taea o calcification o te ganglia basal - wharanga whanau.

tikanga rangahau mō te tātaritanga

I mua i te putanga o te tūroro CT Nōna ka rangahau radiological o te roro. Ngā mihi ki te haerenga mai o tikanga hou o te rangahau, kua riro tohunga whakapakoko atu kōrero i te wāhi kua pā. Heoi, kia tuhia te reira e te tūtohutanga teitei mo te pikitia haumanu hoatu he rorohiko, nui atu i te atahanga te kōwarotanga autō. I roto i te tātaritanga o te nuinga o ngā pikitia e whāiti wāhi pānga ki te ORB koma. He iti i roto i te rahi ratou. Nuinga o ngā wā mamae huringa i roto i te basal ganglia, thalamus, roro tuarongo. Ko te taumata o te calcification huri noa te taua e te taitamariki e i roto i te paari. rerekētanga i kitea ano i waenganui i te rōpū, i roto i nei te mate, ko te asymptomatic Farah, me te hunga i reira tahi te syndrome e tohu korerotia.

akoranga histological

I roto i te whakamātautau pou-tūpāpaku i roto i te āhuatanga roro ko e whai ake: oko i te ahua te repa (etahi pae pekapeka). A, no te mo te maripi hanga e ratou he reo rite te chestnut. Hoki tātaritanga histological o ngā tauira unuhanga whakamana te: Ko te wāhanga o te uho haaparuparu, ganglia basal, roro tuarongo. Ko roto i puta te calcification whakamutunga tino maha. Ko nga tauira o tai konupūmā reira. Ano, atu pinepine e tāutuhia ratou i runga i te pera (iti, reo), te tōiti. Iti noa (take katea) mate Farah patua te rua. Puta noa i te roa o te oko, me te i roto i te kopa e karapoti kitea conglomerates konupūmā i roto i te rahi iti. i roto i te kopa hoki taratahi aroaro o tohu o te ateneke, konumohe, konukurahina, mucopolysaccharides.

tātaritanga

Tei runga i ranei nga tohu mate o Farah, kia utrudnyatsya torutoru tātaritanga. E mea pinepine te pāngia reira e tupono, haamau'araa atahanga ki te whakaū i te mate katoa rerekē. Tuatahi o te katoa, e kore e te tohunga ofati te pākia o te konupūmā me te tahi atu malformations. Na ka whakaritea ki te tomography computed (ranei whakamātautau X-ray). Doctors mōhio e tetahi o nga raruraru i roto i te tātaritanga tika he hypoparathyroidism. Ko te mate, e puta ka te hē o te ira parathyroid. Nō reira, makaka te taumata toto konupūmā, a kei te piki haere te taumata ūkuikui. Ki te kitea te karapa CT te hanganga calcification striopallidozubchatyh, ka ki te wehewehe i hypoparathyroidism i te huru pērā i te mate Farah, atu tätari. Tuatahi o te katoa, he mea nui ki te whakatau i te taumata o te taiaki parathyroid me te konupūmā. whakamahia hoki i roto i te tātaritanga o te hinga Parasitic o te pūnaha io. tauhohe Specific puta i roto i te toto, inu cerebrospinal. Varavara, rerekëtanga te headlamp mate ki taua huru rite Bourneville sclerosis.

maimoatanga

Te tango nohanga konupūmā, i hanga e nei i roto i nga oko roro, me te toto, e taea. Ka rite ki te tikanga, he symptomatic te maimoatanga o tenei mate. Tuatahi o te katoa, kua hāngai te reira i te whakapai ake i te pākia o te konupūmā me te ūkuikui i roto i te tinana. Ki te kitea nga tohu mate o Parkinson, whakatakoto te mātanga taero motuhake (levodopa). hoki Farah mate, te maimoatanga o ona mau faaiteraa, e aofia i te horomanga o antioxidants, māngai mō te whakapai ake i pākia. Maimoatanga o blockers hongere konupūmā he hua. Ko reira utu whakaaro i te meka e ko te onge, me i matau painga te mate. I roto i te nuinga o te wā, therapy ko ki te hiki i ngā tohu faaiteraa o te mate, engari e kore e te te tohu o te calcification pāngia.

Haurangi i te mate headlamp

Mai takahi ana i tenei huru te pākia o te roro, me te tai konupūmā i te pānga irritating i runga i tona kikokiko, he pai rangirua te mate Farah matapae. āta kauneke te mate ki te tau, ake i putunga konupūmā. O te akoranga, e kore e tenei katoa tupu i roto i te tau kotahi. Ko te tikanga, i mua mate neurodegenerative i runga i te maha o ngā tekau tau. Ko te raruraru matua ko te kore o te mōhiohio i runga i te āhua, me te te ngaro o te maimoatanga motuhake. Na reira, e hāngai therapy i te whakapai ake i te kounga o te ora o te manawanui. pāngia kino mate i roto i te tīmatanga o te wāhanga - tetahi atu wāhi kino.

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