HauoraDiseases me ngā Here

Mate o Rasmussen (encephalitis). Ngā take Rasmussen syndrome

no te mate o Rasmussen ki te kāwai o onge mate inflammatory whawhati i roto i te roro. Ka puta mai tēnei encephalitis i roto i ngā tamariki i raro i te 15 tau. Nuinga o ngā wā, pāngia te mate i roto i te pakeke. I roto i te taiohi me ngā pakeke, ko te tino onge tenei ahua o te encephalitis.

Ko te tukanga, ka uru tetahi te tahi atu tuakoi o te roro ranei. Ka rite ki te mate kauneke, kite tākuta reira atrophy ahu whakamua. tohu Doctors ki te ātete tino ki maimoatanga mate. I roto i te meka, te mate Rasmussen - encephalitis ki ngā āhuatanga motuhake e kore e taea te ora.

take pea encephalitis Rasmussen

Whakatika kua kore i whakapumautia ra ano te etiology o te mate. Scientists tāutuhia anake e toru ngā āhuatanga matua e taea te kōkiri me te paturu i te ahunga whakamua o te huru pathological puta i roto i te pūnaha io pokapū. He plurality o rata whakapono e meinga Rasmussen syndrome e paturopi autoimmune, huaketo me te cytotoxic T-lymphocytes.

tūranga pea o cytomegalovirus, i tawhiti i te uho kaka o tūroro pakeke. Ko reira taea e meinga enei tukumate mumura, whakawhanake ki te mate mahu. I tua atu, e taea te Nā reira puta pōauautanga i muri i mate i mua.

Na, te nuinga o kaipūtaiao whakapono e ko te reira he paturopi autoimmune take encephalitis Rasmussen. Ko te take o te mate e whakapono hoki ki te kia faataa e cytotoxic T-lymphocytes.

I roto i te tūroro ki te syndrome o Rasmussen, e te tahi mau taime kitea i roto whanaunga e mamae i te tahi atu mate autoimmune. Hei tauira, te mate o Behçet. fokotu'u tenei te whakapae e kua whai wāhi whanaunga i roto i te tukanga pathological āhuatanga ira noa. I roto i ngā, tuku reira ki āhuatanga pērā i Hľa-galotipy.

Tohutanga entsifalita Rasmussen

I te tīmatanga, faaite te mate haurangi nekeneke rahi. Ka rite ki nga whakaeke mate kia uru myoclonus rohe. Neke atu i te wa, kaha nga whakaeke. E haere tahi ratou e mamae uaua, mate o te mahara, me te hinga. E mea pinepine, e fehangahangai tūroro ki whakaeke i roto i te moe.

Ahu, faaite te mate ano mate o te kaha me te kōpā wāhanga tupu i roto i tetahi wahi o te tinana. whakaatu Studies he hekenga i roto i te mahi i roto i te wāhi roro kua pā.

tātaringa

Tohu korerotia i roto i te iwi e mate ana hoki te tau, me te syndrome o Rasmussen. Encephalitis ki te etiology o ngana ki te tautuhi rite wawe rite taea. Tenei taea ki tatou tumanako mo te pānga pai o te therapy immunosuppressive. Na i haere tuatahi o katoa ki te ako o haumanu, whakamana MRI ko Tirohia te te.

Methods o te maimoatanga o te encephalitis o Rasmussen

No te mea na tawhiti i reira he tautohe e pā ana ki te take o te syndrome o Rasmussen, e kore encephalitis tukinotia e te tikanga tikanga. Ki te whakahau kite wawe o te mate pūāhua rongoā antiepileptic. Tūtohu i te kai hangaia ki te whakapiki ake i te kai o kai taonga i roto i te ngako, me te whakaiti i roto i te nui o ngā kai kai kei roto warowaihā. E mea pinepine kitea reira whai hua ki te whakamahi i plasmapheresis, corticosteroids, immunoglobulins.

E mea pinepine, kua haere te maimoatanga o te mate ki tikanga tuwhena. Tūroro e kua tukua te ma'i rahi, me te whara roro matatini, he mea e tika ana ki te mahi i huaranga o ngā pūtau io. Na rite noa ki taea tamata tatou kore ki te whakahaere i craniotomy.

I te tahi taime whakaekea tūroro wawaotanga hāparapara - Hemispherectomy. I muri reira māmā mō te syndrome o Rasmussen. Encephalitis, o te akoranga, rau ona tohu, paresis korerotia raruraru ki kupu ranei. Heoi, patu he iti noa te manawanui.

Hei hoatu ake pokanga kore he minaminatia, ahakoa te meka e kore e arahi reira ki te whakaoti i whakaora. I muri i te katoa, te whanaketanga o te mate aggravates takarepa neurological tamau, ki nei i reira he retardation hinengaro , me te pāpāngia.

I roto i te wā o pāpaka më o te roro (tuakoi e rua) matapae kāore kino. Kēhi o te mate i roto i tūroro ki encephalitis Rasmussen e kore te nohinohi te.

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