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Gravis Myasthenia: he aha te mea te reira? Take, Tohu me Methods Treatment

Myasthenia i huaina mate tahi nei e nui haere ngoikore uaua. I whakaahuatia tuatahi te mate rite i roto i te 1672. E ai ki ngā tatauranga, e kore e tenei mate puta maha rawa. Otiia, e hiahia ana i roto i ngā pātai e pā ana ki aha i reira ko te tane maha iwi, he aha te mea reira me aha nga tohu i aru. I muri i te katoa, Tei tātaritanga wawe talena me te kounga o te ora o te tangata e mate ana.

Myasthenia gravis - he aha te mea te reira? Ko te take o te mate

Ki te he noa nga mea katoa, acetylcholine ki runga ki excitation tomo ki te kapiti synaptic, e mahi i runga i receptors motuhake i roto i te uaua membrane - kupu whakaongaongatia te me whakaiti o muka uaua. Otiia i roto i nga kohungahunga, he whati tenei tikanga o te tuku o te pana io.

Tonu ko reira ia tapao e gravis myasthenia - he mate ira. A faaoti i teie mahana ki te tohatoha e rua momo taketake o tona whanaketanga. I roto i ētahi wā, e pā ana te kore i roto i te tuku o te karere hihiko te ki te rangirua o te mahi noa o te hypothalamus. Ko tētahi atu take noa o te mate ko te lesion autoimmune o te repe thymus, e arata'i ki whakaiti i roto i te moni synthesized acetylcholine.

He he gravis he myasthenia fā'ele'i pera-ka karanga. He aha te mea te reira? Ko tēnei puka o te mate puta i roto i whanau hou, ki te mamae o ratou whaea i disorders o kawenga uauaio.

Tohu o te mate e taea faaite mai rite i roto i te ra tuatahi i muri i whanau, me i roto i te atu pakeke. He etahi āhuatanga mōrearea e taea meinga gravis te myasthenia whakawhanake. Ko te take mo te whawhai o te uaua ngoikore e taea e tika ki te ahotea nui, te ahotea manavasii, mua mate hopuhopu, me disorders o te pūnaha ārai mate.

Ko te tohu matua o te myasthenia gravis

Ka rite ki kua whakahuatia, ko te āhuatanga matua o te mate, ko te uaua ngoikore. I roto i te ata, tūroro te tikanga ite maitai noa. Ko te torutoru haora i muri i te uaua kōhiwi whiwhi ngenge, ka mutu te mahi, ki runga ki te whakaoti i pāpāngia. I muri noho te kaha ki te whakaiti ora ake.

Tei runga i te raru ko rōpū pānga te wehea ki toru ngā momo matua o te mate:

  • Tino maha, ka pā te mate ki nga uaua, e kua innervated e raru cranial. Na te āhuatanga matua i roto i tenei take, ko te ptosis. Ki te taea okioki te tangata tino whakatuwhera koutou kanohi, na, i muri i te tahi haora, i reira te mea he kua tukua iho äta o te kamo runga.
  • He he ano hoki gravis bulbar myasthenia. He aha te mea te reira? tahi ana tēnei mate e pakaru o te tuku karere hihiko ki te uaua, i te hunga kawenga i roto i te horomia, ngaungau me etahi atu tukanga. Tūroro o te iwi i raruraru ki kai, me te he huringa āta o te reo, tae noa ki tona ngaro oti.
  • I roto i te puka tino whānui o te mate e pāngia, i roto i nei e pāngia nga uaua kanohi tuatahi, ka puta te tukanga ki te kaki, pito o runga, a na i runga i. D.

Methods o te maimoatanga o te myasthenia

E tano ia tapao e gravis te myasthenia mate he tino mōrearea, me te titau tiaki mohio. Ko te meka ko e te āhuatanga tenei mate e te mōrearea pera-ka karanga, e kua haere tahi e te pāpāngia rangitahi o nga uaua romahā, a ka he te riri tika ki te ora i tenei.

Te maimoatanga whai hua anake ko te whakahaere o te raau taero kei roto acetylcholinesterase - he "Proserpine" me "Kalimin". Taua therapy whakamutunga mō ngā tau, me te horopeta o rongoā te rerekē haere tonu i runga i te āhua me te tere o te whanaketanga o te mate rānei. Ki te whakawhanakehia myasthenia gravis ki te whakamārama o te puku o te repe thymus, whakamana pokanga te ki te tango i te tinana.

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