Tenei mate whakaata ngaro

Te nuinga o te iwi nui, e korero e pā ana ki te ngakau, hoatu he ringa ki te taha ki maui o te pouaka. Heoi, i roto i 1643 te taote Itari Marco Severino whakaahuatia te take tuatahi i roto i te aamu o te ngakau ki te matau, ka muri whakaahuatia te 50 tau anō i te wā tuatahi te transposition tonu o whekau, e mohiotia ana ko te mate whakaata. I roto i tenei mate, te wāhi o te whekau ko te ahua whakaata o noa. Na, ko te ngakau ki te matau, te reira anga ano te matamata o te matau, ko te matau, me te puku, engari te tōngāmimi au me te ate, i runga i te anga ke, ki te maui. Whēkau, toto me te te tīpona oko, e whakaritea ana hoki raru i roto i te whakapakoko whakaata. pa te reira i te syndrome whakaata me te marama ngali hangarite: e 2 matamata, me te maui te tika - 3.

O te akoranga, paanga i roto i tenei Pākatokato kikokiko, ka anga te iwi ki te titiro hoki ona take. I roto i te mate whakaata Anotau pēnei rite whanoke rewera me mau horo'a atua. I anake nui i muri, kua kitea e te reira i pūtaiao he whakamārama mō tenei āhuatanga ngaro , a herea ana e ia ki tuatahi dyskinesia ciliary me syndrome Kartagener. I roto i te whānui, i te syndrome whakaata - he mate ira determenirovannoe e pā ana ki waimaero mahi ciliary epithelium tika ki te Morphology koha congenital. I tenei māuiuitanga puta ngā irakētanga i roto i 12 ira rerekē e whakawaehere te kōtuitui o te pūmua e hiahiatia ana mō te hanga me te ciliary mahi tika. Ka rite ki te hua, tūroro i disorders te whakararuraru, Respiratory rite rere uaua o hūpē i te wahi romahā, a i roto i nga tangata (uaua wahine) hoki pākoko auau.

I roto i te whanaketanga embryonic o te kukune ko te kaupapa o te makawe iti tautuhi te tuaka e pā ana ki i te ripa mana, a no te mea, i roto i te mutunga, i roto i te ofatiraa o te mahi o ngä makawe puta tranpozitsii. Ka rite ki te nuinga atu abnormalities ira, āhuatanga mate e te whakaata autosomal aratau ngoikore o tupu, engari no te mea he tino iti tona auau: anake i waenganui i te 1 i roto i te 10,000 ki te 1 i roto i te 60,000.

I te tahi taime, i roto i te āhuatanga tino uaua, i reira he transposition oti o whekau: E kite ana ratou, engari kei te mahue tonu te ngakau. I roto i te 95% o ngā take, tenei tūroro Morphology mamae ngā hē ngakau congenital. Ko te tahi atu take, te syndrome whakaata, reira kua tata kore pūtaiao kï pānga i runga i te hauora, te kounga me te roa o te ora. Taea anake etahi hūhi i te meka e te iwi e te tikanga mōhio o tenei te āhuatanga, engari no te mea i roto i te hui o te raruraru hauora tākuta i reira e nui i uauatanga titiro tuatahi ki te tātaritanga o mate.

Heoi, kua whakaaetia te taumata o te whanaketanga o te rongoā o nāianei rata ki te tātari kore anake transposition o whēkau i iwi, engari ano hoki ki te mahi i te tātaritanga ira ki te tāutu i ngā irakētanga i roto i te ira ūnga. Ko te raruraru matua e kia fehangahangai iwi ki te tātaritanga o "mate whakaata" - he okana transplantation. Nā ki te rarity o te mate, kitea he uaua te kaituku pea, a maha e kore e titiro taea.

E tano ia tapao i te meka i kitea te inversus Pae e kore anake i roto i te tangata, engari ano hoki i roto i nga māngai o te ao kararehe, pērā i ngata. Na, ngata, rite ki te tikanga, kua he totohu, whiria ki te tika, engari ki te auautanga o te 1 ki te 10000 - 1 ki te 100000 he mau taata e whai i te totohu, whiria ki te maui.

I tua atu, mate o te whakaata ko te whenua pai mo te whanaketanga o fakafa'ahikehé. Ahakoa te meka e kua roa hinga te Anotau ki te warewaretanga, whakapono maha iwi tonu e ki te Pae inversus tūroro riro mana tipua, me te pūtaiao e pā ana, i roto i te tahuri, tonu ki ako anaanatae te āhuatanga meinga he taua irakētanga motuhake o te huinga ira.