Rhabdomyosarcoma Embryonal: maimoatanga, waitohunga

e pā ana Rhabdomyosarcoma ki te puka o te sarcoma - mate pukupuku kiko ngohengohe, wheua kiko tūhonohono ranei. Ko te nuinga pea, ki te puta i roto i te uaua piri ki nga wheua te puku. Rhabdomyosarcoma - repara e ahu i roto i te uaua kōhiwi. tīmata ratou i roto i te wahi i tetahi i tetahi o te tinana ranei i roto i te maha o nga wahi.

Microscopically rhabdomyosarcoma i roto i ngā pakeke e te puka o ngā pūtau elongated porotaka ranei rerekē. Ētahi atu āhuatanga o tenei puku o tamarikitanga.

momo o te rhabdomyosarcoma

E wehewehea Rhabdomyosarcoma o te hanganga ā-ki momo:

1. pūtau rhabdomyosarcoma Embryonal ngā o tawhio me fusiform nei tūhuratanga cytoplasm whakaatu he striations roa hake ranei. puta tenei momo o te rhabdomyosarcoma atu pinepine. puta te reira i rhabdomyosarcoma embryonal i roto i ngā tamariki, me te taiohi. Kei roto i te kaki upoko ranei, i runga i te kikokiko, i roto i te awa ihu. Ko te tūtohutanga o te pukupuku ki radiation therapy, engari he e pängia ana ki te matahoki tere.

tito 2. kauae rhabdomyosarcoma te o te rōpū o ngā pūtau tawhio me porotītaha, e kua karapotia e te septa o kiko tūhonohono. Hoki tenei momo o te pukupuku āhuatanga e te ahua i runga i nga waewae ranei ringa, puku, uma, whakaeneene ranei whekau taihemahema. Pinepine e taea te kitea i te reira i roto i ngā taiohi me ngā pakeke i runga i nga wahi. he rawakore waitohunga.

3. Composition rhabdomyosarcoma pleomorphic - Polymorphic muka-āhua, rīpene-rite, whetu-āhua pūtau o te puku i kia puta i runga i nga waewae ringa ranei o te iwi. Ka rite ki te tikanga, hohoro tupu rhabdomyosarcoma puta a e kore e meinga te mamae me disorders mahi. puta te reira i uaua anake. Ratou maha tupu i roto i te kiri, me te hipoki ki te tuwhenua, hanga exophytic, toto puku.

āhuatanga mōrearea

I roto i te āhuatanga taiao kitea taua, e whakanui i te tūponotanga o te takanga o tenei puku. rerekē ana tēnei i te nuinga o te mate pukupuku rhabdomyosarcoma.

Nā ki te meka e kore te e mohiotia rite take o te whanaketanga puku, e kore e taea te hoatu e tatou tetahi tohutohu mō te te haapae tona hanganga. Heoi, e ti'a ia tatou mau i roto i te ngakau e ki e tika maimoatanga o te tūroro ki te rhabdomyosarcoma taea ētahi wā te tino ora.

āhuatanga Risk mo te ahua o te rhabdomyosarcoma embryonic e taua mate ira fakapapau'i:

1. Li-Fraumeni syndrome ko te mate onge i roto i enei i riro i huru, kino ira ka ngaro tetahi matua ki te auau teitei whakatika momo puku kanorau. Riro i roto i tenei māuiuitanga tuku pū o tauhohe kiko puku ka tino whakanuia ana te tūponotanga o te whakawhanake i te pukupuku i te wawe tau (30 tau).

2. neurofibromatosis momo tuatahi - te mate tino noa riro e ai te ahua o te predisposition ki repara.

3. Syndrome Beckwith-Wiedemann - māuiuitanga, āhuatanga nei i te macrosomia, macroglossia me omphalocele. Ko reira ano hē kitea i roto i ngā tamariki a te taiepa mua o te puku, whaturama, hypoglycaemia fā'ele'i, te hahiraa o te uaua kiri taupoki.

4. Costello syndrome - he mate onge, āhuatanga nei i te malformations congenital: retardation tupu, makaka āhuatanga kanohi, huringa kiri.

5. syndrome o Noonan - he mate iranga āhuatanga e poto roa mo e te ine, me te i roto i te whanaketanga somatic. Ka taea e puta te reira i roto i te utuafare e aore i roto i tetahi o ona ngā mema.

ake i ta etahi pēpi nei i taimaha whanau me te tupu, kua, te mōrea o te rhabdomyosarcoma embryonal. Ka rite ki te tikanga, Heoi, nga take o te rhabdomyosarcoma embryonal he unknown. He tohu o te mate ko te ahua o te puku hoko atu me te ake.

tohu

whakaritea tohutanga o te mate o te mate pukupuku te. E hiahiatia ana tonu kōrero te tākuta, ki te mea kua whakarārangitia tamariki tohu o te mate pukupuku:

• edema ranei ngawhatanga, te whakanui ake i roto i te rahi ranei e kore e haere, i ētahi wā mamae;
• kanohi kua ngawha;
• ānini nui;
• uaua ki te defecation me urination;
• toto i roto i te mimi;
• toto i roto i te tōu, ihu me te korokoro.

tātaringa

Ki te rā, whakawhanakehia tikanga mō te whakatau rhabdomyosarcoma noa ona tohu mārō rawa tuatahi.

Ko te tohu tuatahi o te mate pukupuku - tetere rohe induration ranei, e kore e meinga raruraru i te tuatahi te mamae ranei. He huru o rhabdomyosarcoma, ringa, waewae, me te utumu tenei tohu.

Ki te paetata te puku kei roto i te rohe puku papatoiake ranei kia meinga puku mamae, ruaki kōroke ranei. Te reira i rhabdomyosarcoma embryonal o te wāhi retroperitoneal. More uaua, te whakawhanake i roto i te wahi biliary, rhabdomyosarcoma ai jaundice.

Ki te reira te mea he māharahara o tenei puku, he mea e tika ana ki te whakahaere i te unuhanga, e ka whakapūtā he aha te ahua o te rhabdomyosarcoma ahu.

I roto i te nuinga o te wā, whakatika rhabdomyosarcoma i roto i ngā wāhi i reira te ngāwari kitea reira, hei tauira, te kōhao nasal waho te Afio ranei. Ki te puta te kanohi kua ngawha, secretions nasal ranei, kia kōrero tonu koe i te tākuta ki te puku whakapae ki te kia pāngia i te wā wawe o tona whanaketanga. I roto i te take i reira puta rhabdomyosarcoma i runga i te mata o te tinana, kei te ngāwari kitea reira, kahore te tūhuratanga tino. Tenei kiko ngohengohe rhabdomyosarcoma embryonal pera-ka karanga.

I roto i te 30% o te tūroro ki te rhabdomyosarcoma embryonal e i te wā wawe ka taea te tino nekehia atu te reira. Ko te nuinga nui o tūroro ngā whakamātautau heheu metastases iti, maimoatanga o e titau te aroaro o te hahau.

rhabdomyosarcoma Embryonal, e kua kei roto i te rohe raho maha hua i roto i ngā tamariki iti, ka kitea ngā mātua o te tamaiti, ka horoi. Ki te puta te pukupuku i roto i te mimi, meinga ratou uaua i roto i te urination toto rere ranei - tohumate e kore e taea te waiho.

atamira puku

1. Ko te mahi tuatahi. pea te puku i tetahi rahi, engari kua kore e takahia ai ki nga taikiri o te pūnaha, me te e kei i roto i tetahi o nga wāhi prognostically pai o te tinana:

- kanohi wāhi periocular ranei;

- upoko me te kaki (hāunga kiko i roto i te roro, me te wāhi ua);

- aerodynamics te ate, me te kawa tōngāmimi;

- i roto i te kōpū komurumurua ranei.

Places waho te whakarārangitia, e whakaaro ngā wāhi kino.

2. Ko te wāhanga tuarua. Pupuhi Ko tetahi o nga rohe kino (rohe e e ngaro i roto i te pai). rahi puku he iti iho i te 5 cm, me te kore i horapa ki te taikiri kua puta.

3. Ko te taahiraa tuatoru. Kei te puku kei te i roto i te wāhi kino, a ka whakatau i tetahi o nga tikanga e whai ake nei:

- te rahi o te puku iti iho i te 5 cm, a ka wherahia ana e ia ki runga ki te taikiri muri;

- Ko nui atu i te 5 cm te puku, me i reira ko te mōrea e ka horapa ki te kōpuku tīpona tata.

4. tuawha te atamira. Ka taea e te rahi puku e tetahi, a ka wherahia ana e ia ki te taikiri i muri. Kua he horapa o te mate pukupuku ki ngā wāhi tawhiti o te tinana.

rōpū mōrearea

rōpū mōrearea manawanui whakaritea whakatau te tūponotanga o te hohokitanga o rhabdomyosarcoma. Me riro i tetahi tamaiti e te manako maimoatanga i rhabdomyosarcoma embryonal, hahau atu ki te riro iti tūponotanga o puku hohokitanga. Tirohia raau anticancer, inenga me te maha o ngā wā - takoto tenei katoa e te mōrea ki tetahi tamaiti tuku - iti, takawaenga tiketike ranei.

kōwhiringa maimoatanga

Ka taea te tukinotia tūroro ki rhabdomyosarcoma embryonal i roto i ngā huarahi rerekē.
Treatment tā puku mārere tikanga motuhake whakaaro nei ki te kia tuku iho. kei raro i te mau tamataraa haumanu Ētahi tikanga. Kua haere tamataraa haumanu ki te whakapai ake i ngā tikanga tīariari o te rongoā te whakanui ake i te nui o ngā raraunga o te tikanga hōu o te rongoā tūroro ki rhabdomyosarcoma ranei. Ki te rite ki te hua o te mau tamataraa haumanu, puta reira e e hau ki tuku iho nga tikanga hou o te maimoatanga, haere te maimoatanga hou ki te kāwai o tuku iho.

Mai te pukupuku mārere ahu ki te puta i roto i ngā wāhi rerekē o te tinana, pā he maha nui o maimoatanga. Maimoatanga o te rhabdomyosarcoma i roto i ngā tamariki te mātakitaki e te matepukupuku rānei pediatric.

I roto i nga tikanga o te maimoatanga, i reira e etahi e taea meinga pānga taha, ara ka haere te maimoatanga mai i te wa roa.

pokanga

tikanga hāparapara, tango o te puku ranei, Kei te whānui whakamahia i roto i te maimoatanga o te rhabdomyosarcoma. huaina ana tēnei mahi ko te "excision rohe whānui". Tenei pokanoa Ko ki te tango wahi o te puku, me te kikokiko e karapoti ana tahi me taikiri e hoki pā rhabdomyosarcoma. Treatment ētahi wā ko te ki te mahi i te maha ngā mahi. Ko te whakatau i runga i te whakarite o te mahi, me tona momo tei runga i te āhuatanga e whai ake nei:

- te waiho i te wāhi taketake o te puku;

- mahi tetahi tamaiti o te tinana pāngia e te puku;

- puku whakautu ki te iraruke hahau ranei, e taea te whakamahi i runga i te kaupapa matua.

e kore te mea te nuinga o te tango o te rōrahi katoa o te puku i te pokanga o te tamariki ka taea.

whangai ana Embryonal rhabdomyosarcoma kiko ngohengohe ki te kia i hanga i wāhi rerekē o te tinana, ia o nei titau ona ake mahi. tohua wawaotanga hāparapara te i roto i te take o kikokiko rhabdomyosarcoma kanohi ranei, ki te whakau i te unuhanga te tātaritanga. I mua i taea te mahi kia whakaritea ki te hahau iraruke ranei ki te whakaiti pukupuku nui, e kore e taea te whakahaeretia i runga i, ki te faaohie i te mahi o te tango i te mate pukupuku.

Ahakoa, ki te kore e taea e te tākuta te tango i te puku katoa, kia pehi e tūroro i te mutunga o te mahi ki te hahau ki te pehi i ngā pūtau mate pukupuku ki te noho ora. Āpiti atu ki te hahau, whakamahia radiation therapy te. i huaina Treatment hāngai ana te whakaiti i te mōrea o te hohokitanga o te mate te therapy adjuvant.

therapy radiation

Ki tenei momo o te maimoatanga whakamahia X-ray atu radiation ranei. whakahaua radiation therapy i te tahi mea, kia whakamatea pūtau puku ranei ki te mutu tona tupu. Kua kitea e tōna tono i roto i te rongoa e rua ara ki te iraruke - waho, me te ā.

Ka whakamahia e waho he pūtake radiation i waho te tinana tangata mo irradiating te puku. therapy radiation ā-brachytherapy ranei irradiates puku ki te whakanohonga o ngā matū iratuki i roto i te takiwā tonu o te roto o te tinana tangata. Kei te whakamahia te reira ki te hamani mate pukupuku tōngāmimi, pane me te kaki, repeure, teke.

Momo o te radiation therapy me horopeta whakaritea e te tau o te tamaiti, me te momo o te puku, tona localization tuatahi engari ano hoki te aroaro o te puku wäriu me te tohu o te puku whakauru tata taikiri i muri i te pokanga.

hahau

Tenei ahua o te maimoatanga mate pukupuku e whakamahi rongoā ki te aukati i te tupu o ngā pūtau mate pukupuku. taero hahau āwhina patua enei pūtau ranei ki te karo i to ratou wehenga. E tangohia te raau taero hahau pūnahanaha waha ranei patia e pâmuhia intramuscularly ranei. Tae i roto i te toto, pā taero pūtau mate pukupuku, puta noa i te tinana. A, no te e patia tika drugs hahau rohe ki whēkau me kōwhao tinana, kia rite ki te pai kia rite i roto i te inu cerebrospinal. Kei te maha whakamahia huinga hahau, i te mea he maimoatanga e whakamahia e te neke atu i te kotahi tarukino anti-mate pukupuku. tīpakohia tikanga hahau te i runga i te momo, me te wāhanga o te whanaketanga o te neoplasm rānei.

whakaaturia hahau te ki te tamaiti katoa e te tukinotia hoki rhabdomyosarcoma. āhei te reira ki a koe te whakaiti i te tūponotanga ka o mate hohokitanga. Ko te kōwhiringa o te rongoā, te horopeta me te maha o ngā tukanga tautuhi rōpū mōrearea rhabdomyosarcoma.

maimoatanga New

momo New o maimoatanga rhabdomyosarcoma, haere i te whakamātautau:

• pota nui o hahau i roto i te taha ki te whakahaere i transplant kakau pūtau. hanga te tikanga e taea ki te whakarite i te whakakapinga o te pūtau hematopoietic e kua ngaro i roto i te maimoatanga mate pukupuku. E nekehia atu pūtau toto teeki mua ki te maimoatanga o te wheua wheua toto ranei o te manawanui, me te tiaki. Na roto i te mutunga o te hahau raskonserviruyut pūmau pūtau kakau, ka hoki ki te manawanui i te whaowhia. Ko te kupu ki nga pūtau toto whanga.
• Immunotherapy. A, no te ki tenei ahua o te maimoatanga whawhai mate pukupuku te whakamahi i te pūnaha ārai mate o te manawanui. taero e whakahaeretia ana e ki te whakapai ake whakahoki nga pa tūturu ki te mate pukupuku ranei. huaina ana tēnei maimoatanga ko biotherapy o te pukupuku.
• therapy hāngai. whakahaua tenei momo o te therapy te ki metastasis. hāngai therapy hāngai te i runga i te whakamahi o paturopi motuhake e herea ki ngā pūtau mate pukupuku. He rite ki te paturopi tikanga o te tinana tangata enei he paturopi. Ko te kupu tohu ratou he tarukino tiketike-tech. Ngā mihi ki te therapy hāngai i roto i te maimoatanga o "matū" Ka taea te kitea ki te patu i ngā pūtau mate pukupuku anake, kahore tükino pūtau hauora. A, no te rhabdomyosarcoma i roto i inhibitors angiogenesis e whakamahia rite ūnga therapy. Enei taero ārai i te hanganga o oko toto i roto i te pukupuku. arata'i tenei ki te meka e te pohe a'era puku me tūnga tipu. inhibitors Angiogenesis me paturopi monoclonal - momo o āpiha pangia tamataraa haumanu mō te whakahaere rhabdomyosarcoma embryonic.